Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children19710.24287/1726-1708-2018-17-3-111-119LITERATURE REVIEWОБЗОР ЛИТЕРАТУРЫMorphological diagnosis and assessment of the malignant potential in pediatric adrenal cortical neoplasmsОсобенности морфологической диагностики и определение злокачественного потенциала адренокортикальных опухолей у детейhttps://orcid.org/0000-0002-8552-7682KletskayaI. S.КлецкаяИ. С.
Russian Federation

Iryna S. Kletskaya, MD, pathologist

119571, Moscow, Leninsky prosp., 117

Клецкая Ирина Семеновна, врачпатологоанатом патологоанатомического отделения 

119571, Москва, Ленинский просп., 117 Тел.: +7 (964) 556-20-51

ikletskaya@gmail.comhttps://orcid.org/0000-0003-0777-9152RogozhinD. V.РогожинД. В.
Russian Federation
https://orcid.org/0000-0001-7732-8184KonovalovD. M.КоноваловД. М.
Russian Federation
https://orcid.org/0000-0001-5461-7442EktovaA. pЭктоваА. П.
Russian Federation
https://orcid.org/0000-0002-0511-8222KushnirB. L.КушнирБ. Л.
Russian Federation
Russian Children's Clinical Hospital of Pirogov Russian National Research Medical UniversityРоссийская детская клиническая больница ФГБОУ ВО РНИМУ им. Н.И. ПироговаDmitriy Rogachev National Medical Research Center of Pediatric Hematology, Oncology, ImmunologyФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева»Russian Medical Academy of Postgraduate EducationФГБОУ дополнительного профессионального образования «Российская медицинская академия непрерывного профессионального образования»240920181731111192409201824092018Copyright ©; 2018, «D. Rogachev NMRCPHOI»Copyright ©; 2018, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2018«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/197

Adrenal cortical neoplasms in pediatric population are very rare. The clinical manifestations and biological behavior can be different from their counterparts in adults. This review contains data of epidemiology, clinical features, histology, biological behavior of adrenal cortical neoplasms in adults and children with particular attention to the approaches to malignancy assessment in different age groups.

Опухоли коры надпочечников у детей встречаются редко. По клиническим проявлениям и биологическому поведению они отличаются от аналогичных опухолей у взрослых. В настоящем обзоре литературы представлено сравнение эпидемиологии, клиники, гистологического строения и биологического поведения опухолей коры надпочечников у взрослых и детей, особое внимание уделено подходам к определению злокачественности этих опухолей в разных возрастных группах.

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