Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children23010.24287/1726-1708-2019-18-1-88-95CLINICAL OBSERVATIONSКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯB-cell lymphoma is unclassifiable, with signs intermediate between diffuse large-cell B-cell lymphoma and Hodgkin lymphomaВ-клеточная лимфома неклассифицируемая с промежуточными признаками между диффузной крупноклеточной в-клеточной лимфомой и лимфомой Ходжкинаhttps://orcid.org/0000-0002-7846-3473SagoyanG. B.СагоянГ. Б.
Russian Federation

Garik B. Sagoyan - MD, pediatric oncologist Department of clinical oncology.

117997, Moscow, Samory Mashela st., 1

Сагоян Гарик Барисович - врач - детский онколог отделения клинической онкологии.

117997, Москва, ГСП-7, ул. Саморы Машела, 1

sagoyan-garik@mail.ruhttps://orcid.org/0000-0002-3247-8688AnderzhanovaL. Kh.АндержановаЛ. Х.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0002-8725-7532DyakonovaYu. Yu.ДьяконоваЮ. Ю.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0003-3664-2876AbramovD. S.АбрамовД. С.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0001-8129-0545ShcherbakovA. P.ЩербаковА. П.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0002-4779-1896MyakovaN. V.МяковаН. В.
Russian Federation

Moscow

Москва

Dmitriy Rogachev National Medical Research Center of Pediatric Hematology, Oncology, Immunology Ministry of Healthcare of Russian FederationФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России2104201918188952104201921042019Copyright ©; 2019, «D. Rogachev NMRCPHOI»Copyright ©; 2019, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2019«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/230

B-cell lymphoma is unclassifiable, with signs intermediate between diffuse large-cell B-cell lymphoma and Hodgkin's lymphoma (LH), is a rare aggressive lymphoma with an uncertain prognosis that has specific morphological and immunophenotypic characteristics characteristic of both diffuse B-large-cell lymphoma and Hodgkin's lymphoma. In this article, the comparative characteristics of NIVCL and various variants of large cell B-cell lymphomas are presented, as well as a description of the clinical case of NVCL in a child of 3 years. Patient's parents agreed to use personal dats and photos in research and publications.

В-клеточная лимфома неклассифицируемая с промежуточными признаками между диффузной крупноклеточной В-клеточной лимфомой и лимфомой Ходжкина (НВКЛ) - редкая агрессивная лимфома с неопределенным прогнозом, имеющая специфические морфологические и иммунофенотипические характеристики, свойственные как диффузной В-крупноклеточной лимфоме, так и лимфоме Ходжкина. В статье представлены сравнительные характеристики НВКЛ и различных вариантов крупноклеточных В-клеточных лимфом, а также описание клинического случая НВКЛ у ребенка 3 лет. Родители пациента дали согласие на использование информации о нем, в том числе фотографий, в научных исследованиях и публикациях.

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