Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children23110.24287/1726-1708-2019-18-1-96-103CLINICAL OBSERVATIONSКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯHepatosplenic γδ T-cell lymphoma in a 4 years old childСлучай гепатоспленической γδ Т-клеточной лимфомы у ребенкаhttps://orcid.org/0000-0002-3247-8688AnderzhanovaL. H.АндержановаЛ. Х.
Russian Federation

Lily H. Anderzhanova - MD, hematology, Department of oncohematology.

117997, Moscow, Samory Mashela st., 1

Андержанова Лилия Халитовна - врач-гематолог отделения онкогематологии.

Москва, ГСП-7, ул. Саморы Машела, 1

anderliliya@gmail.comhttps://orcid.org/0000-0003-2294-0821FomynihV. V.ФоминыхВ. В.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0003-3664-2876AbramovD. S.АбрамовД. С.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0002-4779-1896MiakovaN. V.МяковаН. В.
Russian Federation

Moscow

Москва

Dmitriy Rogachev National Medical Research Center of Pediatric Hematology, Oncology, Immunology Ministry of Healthcare of Russian FederationФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России21042019181961032104201921042019Copyright ©; 2019, «D. Rogachev NMRCPHOI»Copyright ©; 2019, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2019«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/231

Hepatosplenic T-cell lymphoma (HSTCL) is a rare and clinically aggressive type of T-cell lymphoma that characterized by proliferation in the liver, spleen and bone marrow. The article presents analytical review of literature and the clinical case of γδ HSTCL in 4 years old child. Patient's parents agreed to use personal dats and photos in research and publications.

Гепатоспленическая Т-клеточная лимфома (ГТКЛ) - редкая, агрессивно протекающая периферическая Т-клеточная лимфома, характеризующаяся пролиферацией злокачественных ав или γδ Т-лимфоцитов в печени, селезенке, костном мозге. В статье представлен анализ литературных данных и разбор клинического случая гепатоспленической γδ Т-клеточной лимфомы у ребенка 4 лет. Родители пациента дали согласие на использование информации о нем, в том числе фотографий, в научных исследованиях и публикациях.

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