Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children70510.24287/1726-1708-2023-22-4-134-143CLINICAL OBSERVATIONSКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯCongenital chest wall spindle cell rhabdomyosarcoma in a one-month-old patientВрожденная веретеноклеточная рабдомиосаркома грудной стенки у пациента 1 месяцаhttps://orcid.org/0000-0001-9424-1646UskovaN. G.УсковаН. Г.
Russian Federation

Natalya G. Uskova, Cand. Med. Sci., a senior researcher of Thoracoabdominal  Surgery Group, a pediatric surgeon at the Department of Oncology and Pediatric Surgery

1 Samory Mashela St., Moscow 117997

Ускова Наталья Геннадьевна, канд. мед. наук, старший научный сотрудник отдела торакоабдоминальной хирургии, врач-детский хирург отделения онкологии и детской хирургии

117997, Москва, ул. Саморы Машела, 1

nataliyauskova@gmail.comhttps://orcid.org/0000-0001-8032-9428VystavkinaN. A.ВыставкинаН. А.
Russian Federation

Moscow

Москва

nikavistavkina@mail.ruhttps://orcid.org/0000-0002-5308-6544TalypovS. R.ТалыповС. Р.
Russian Federation

Moscow

Москва

riumych@yandex.ruhttps://orcid.org/0000-0002-1387-209XAkhaladzeD. G.АхаладзеД. Г.
Russian Federation

Moscow

Москва

d.g.akhaladze@gmail.comhttps://orcid.org/0000-0003-0621-191XStradomskayaT. V.СтрадомскаяТ. В.
Russian Federation

Moscow

Москва

stv-sergeeva@mail.ruhttps://orcid.org/0000-0002-9375-7517RoshchinV. Yu.РощинВ. Ю.
Russian Federation

Moscow

Москва

vit1982@list.ruhttps://orcid.org/0000-0002-3704-8783KachanovD. Yu.КачановД. Ю.
Russian Federation

Moscow

Москва

kachanov78@gmail.comhttps://orcid.org/0000-0002-4451-3233GrachevN. S.ГрачевН. С.
Russian Federation

Moscow

Москва

nick-grachev@yandex.ruDmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology of Ministry of Healthcare of the Russian FederationФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России201220232241341431003202320062023Copyright ©; 2023, «D. Rogachev NMRCPHOI»Copyright ©; 2023, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2023«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/705

This article presents a rare clinical case of an infant with congenital spindle-cell rhabdomyosarcoma, demonstrates a combined approach to the patient's therapy, describes in detail the performed reconstructive plastic surgery, analyzes the short-term and long-term results of the treatment with an emphasis on late orthopedic complications, provides a detailed literary review on the topic of the publication. The patient's parents gave consent to the use of their child's data, including photographs, for research purposes and in publications.

В настоящей статье представлен редкий клинический случай пациента грудного возраста с врожденной веретеноклеточной рабдомиосаркомой, продемонстрирован комбинированный подход в терапии, описано выполненное реконструктивно-пластическое оперативное вмешательство, проанализированы ближайшие и отдаленные результаты проведенного лечения с акцентом на поздних ортопедических осложнениях, приведена подробная литературная справка по теме публикации. Родители пациента дали согласие на использование информации, в том числе фотографий ребенка, в научных исследованиях и публикациях.

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