Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children72910.24287/1726-1708-2023-22-2-113-122CLINICAL OBSERVATIONSКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯMycosis fungoides in an 11 year-old child: a case reportКлинический случай грибовидного микоза 113 у ребенка 11 летhttps://orcid.org/0000-0001-7837-6890KorsantiyaM. N.КорсантияМ. Н.
Russian Federation

Maya N. Korsantiya, hematologist

Day Care Facility

117997

1 Samory Mashela St.

Moscow

Майя Нугзаровна Корсантия, врач-гематолог

стационар кратковременного лечения

117997

ул. Саморы Машела, 1

Москва

maya.korsantya@fccho-moscow.ruhttps://orcid.org/0000-0003-3664-2876AbramovD. S.АбрамовД. С.
Russian Federation

Moscow

Москва

https://orcid.org/0009-0007-1387-4208EfimovaA. A.ЕфимоваА. А.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0002-2057-2036PshonkinA. V.ПшонкинА. В.
Russian Federation

Moscow

Москва

https://orcid.org/0000-0002-4779-1896MyakovaN. V.МяковаН. В.
Russian Federation

Moscow

Москва

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology of Ministry of Healthcare of the Russian FederationФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России080720232221131221511202224052023Copyright ©; 2025, «D. Rogachev NMRCPHOI»Copyright ©; 2025, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2025«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/729

   Primary cutaneous lymphomas are quite rare in children. Clinical and histopathological manifestations of these diseases in children differ significantly from those in adults. Due to their rarity and complex clinical presentation, diagnosis may take long time. Mycosis fungoides (MF) is the most commonly diagnosed form of primary cutaneous lymphomas in childhood. There are no clinical guidelines for the treatment of children. Literature data on MF variants in children are scarce; the largest study includes 34 patients who were diagnosed on average 4 years after the onset of the first symptoms. In the present article we describe a clinical case of MF in an 11-year-old child with an 8-year history of multiple lesions of the skin and scalp. The patient's parents gave their consent to the use of their child's data, including photographs, for research purposes and in publications.

   The aim of our article is to demonstrate the problems in the diagnosis of the disease, especially at an early stage, because its symptoms may be similar to those of many common pediatric inflammatory skin conditions.

   Первичные кожные лимфомы довольно редко встречаются у детей. Клинические и гистопатологические проявления этих заболеваний у пациентов детского возраста могут значительно отличаться от таковых у взрослых. Из-за их редкости и сложной клинической картины диагностика может быть очень длительной. Грибовидный микоз (ГМ) является наиболее часто диагностируемой формой первичных кожных лимфом в детском возрасте. Клинических рекомендаций для лечения детей не существует. В литературе данные о вариантах ГМ у детей немногочисленны, наиболее крупное исследование включает 34 пациента, у которых диагноз был поставлен в среднем через 4 года после появления первых симптомов. В данной статье мы представляем клинический случай ГМ у 11-летнего ребенка с 8-летней историей множественного поражения кожных покровов и кожи головы. Родители пациента дали согласие на использование информации, в том числе фотографий ребенка, в научных исследованиях и публикациях.

   Целью нашей публикации является демонстрация проблем в диагностике заболевания, особенно на ранних стадиях, поскольку его симптомы могут быть похожи на симптомы многих распространенных детских воспалительных заболеваний кожи.

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