Pediatric Hematology/Oncology and ImmunopathologyPediatric Hematology/Oncology and ImmunopathologyВопросы гематологии/онкологии и иммунопатологии в педиатрии1726-17082414-9314Fund Doctors, Innovations, Science for Children8210.24287/1726-1708-2017-16-1-62-68СтатьиDifferential diagnosis of congenital cystic neuroblastoma and prenatal adrenal hemorrhage in children of the first months of lifeДифференциальная диагностика кистозной формы нейробластомы и кровоизлияния в надпочечник у детей первых месяцев жизниFeoktistovaE. V.ФеоктистоваЕ. В.
Russian Federation
UskovaN. G.УсковаН. Г.
Russian Federation

Russia 117997, Moscow, Samory Mashela st., 1

+7 (495) 287-6570, ext. 6496

nataliyauskova@gmail.comVarfolomeevaS. P.ВарфоломееваС. Р.
Russian Federation
TereshchenkoG. V.ТерещенкоГ. В.
Russian Federation
KachanovD. Yu.КачановД. Ю.
Russian Federation
ShamanskayaT. V.ШаманскаяТ. В.
Russian Federation
TalypovS. P.ТалыповС. Р.
Russian Federation
GrachevN. C.ГрачёвН. С.
Russian Federation
National Research Center of Pediatric Hematology, oncology and Immunology named after Dmitry RogachevФГБУ «Национальный научно-практический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России, Москва10022017161626810082018Copyright ©; 2017, «D. Rogachev NMRCPHOI»Copyright ©; 2017, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России2017«D. Rogachev NMRCPHOI»ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава Россииhttps://creativecommons.org/licenses/by/4.0https://hemoncim.com/jour/article/view/82

Differential diagnosis of adrenal gland tumor in neonates and children of the first months of life is an extremely difficult clinical task. Most often, it is congenital cystic neuroblastoma or prenatal adrenal hemorrhage. As a rule, it is hard to make the right diagnosis due to absence of clinical presentation and similarity of visualization data therefore sometimes surgical tumor removal followed by histological verification becomes the method of choice. The article presents a clinical case of the adrenal gland tumor in 5-months old boy. Authors discuss the difficulties in the formulation of the final clinical diagnosis.

Дифференциальная диагностика объемных образований в проекции надпочечников у новорожденных детей и детей первых месяцев жизни - чрезвычайно сложная клиническая задача. В данном случае чаще всего речь идет о врожденных кистозных нейробластомах и кровоизлияниях в надпочечник. Как правило, отсутствие клинической симптоматики и схожесть данных визуализации не позволяют четко дифференцировать данные патологические состояния, в связи с этим во многих случаях методом выбора становится оперативное удаление образования с последующей гистологической верификацией. Однако все больше исследователей высказывают мнение о том, что необходимо придерживаться консервативно-выжидательной тактики в отношении детей первых месяцев жизни. В статье представлен случай наблюдения за пациентом с образованием надпочечника, описаны трудности, с которыми столкнулись авторы при постановке окончательного клинического диагноза.

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