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<article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns:ali="http://www.niso.org/schemas/ali/1.0/" article-type="other" dtd-version="1.2" xml:lang="en"><front><journal-meta><journal-id journal-id-type="publisher-id">Pediatric Hematology/Oncology and Immunopathology</journal-id><journal-title-group><journal-title xml:lang="en">Pediatric Hematology/Oncology and Immunopathology</journal-title><trans-title-group xml:lang="ru"><trans-title>Вопросы гематологии/онкологии и иммунопатологии в педиатрии</trans-title></trans-title-group></journal-title-group><issn publication-format="print">1726-1708</issn><issn publication-format="electronic">2414-9314</issn><publisher><publisher-name xml:lang="en">Fund Doctors, Innovations, Science for Children</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="publisher-id">836</article-id><article-id pub-id-type="doi">10.24287/1726-1708-2024-23-3-158-163</article-id><article-categories><subj-group subj-group-type="toc-heading" xml:lang="en"><subject>CLINICAL OBSERVATIONS</subject></subj-group><subj-group subj-group-type="toc-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ НАБЛЮДЕНИЯ</subject></subj-group><subj-group subj-group-type="article-type"><subject></subject></subj-group></article-categories><title-group><article-title xml:lang="en">Fibrocartilaginous mesenchymoma: a case report and a literature review</article-title><trans-title-group xml:lang="ru"><trans-title>Фиброзно-хрящевая мезенхимома: клинический случай и обзор литературы</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0009-0002-2852-6760</contrib-id><name-alternatives><name xml:lang="en"><surname>Karyagina</surname><given-names>A. A.</given-names></name><name xml:lang="ru"><surname>Карягина</surname><given-names>А. А.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><bio xml:lang="en"><p>Arina А. Karyagina - a sixth-year student.</p><p>1 Ostrovityanova St., Moscow 117513</p></bio><bio xml:lang="ru"><p>Карягина Арина Андреевна - студентка 6-го курса.</p><p>117513, Москва, ул. Островитянова, 1</p></bio><email>arina.karyagina@gmail.com</email><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-9375-7517</contrib-id><name-alternatives><name xml:lang="en"><surname>Roshchin</surname><given-names>V. Yu.</given-names></name><name xml:lang="ru"><surname>Рощин</surname><given-names>В. Ю.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><bio xml:lang="en"><p>Moscow</p></bio><bio xml:lang="ru"><p>Виталий Юрьевич Рощин</p><p>Москва</p></bio><email>vitaly.roschin@fccho-moscow.ru</email><xref ref-type="aff" rid="aff2"/></contrib><contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-8578-6572</contrib-id><name-alternatives><name xml:lang="en"><surname>Sidorov</surname><given-names>I. V.</given-names></name><name xml:lang="ru"><surname>Сидоров</surname><given-names>И. В.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><bio xml:lang="en"><p>Moscow</p></bio><bio xml:lang="ru"><p>Илья Владимирович Сидоров</p><p>Москва</p></bio><email>ilya93sidorov@gmail.com</email><xref ref-type="aff" rid="aff2"/></contrib><contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-7732-8184</contrib-id><name-alternatives><name xml:lang="en"><surname>Konovalov</surname><given-names>D. M.</given-names></name><name xml:lang="ru"><surname>Коновалов</surname><given-names>Д. М.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><bio xml:lang="en"><p>Moscow</p></bio><bio xml:lang="ru"><p>Дмитрий Михайлович Коновалов</p><p>Москва</p></bio><email>dmk_nadf@mail.ru</email><xref ref-type="aff" rid="aff2"/><xref ref-type="aff" rid="aff3"/></contrib></contrib-group><aff-alternatives id="aff1"><aff><institution xml:lang="en">The N.I. Pirogov Russian National Research Medical University of Ministry of Healthcare of the Russian Federation</institution></aff><aff><institution xml:lang="ru">ФГАОУ ВО «Российский национальный исследовательский медицинский университет им. Н.И. Пирогова» Минздрава России</institution></aff></aff-alternatives><aff-alternatives id="aff2"><aff><institution xml:lang="en">The Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology of Ministry of Healthcare of the Russian Federation</institution></aff><aff><institution xml:lang="ru">ФГБУ «Национальный медицинский исследовательский центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева» Минздрава России</institution></aff></aff-alternatives><aff-alternatives id="aff3"><aff><institution xml:lang="en">Russian Medical Academy of Continuing Professional Education of Ministry of Healthcare</institution></aff><aff><institution xml:lang="ru">ФГБОУ ДПО «Российская медицинская академия непрерывного профессионального образования» Минздрава России</institution></aff></aff-alternatives><pub-date date-type="pub" iso-8601-date="2024-09-08" publication-format="electronic"><day>08</day><month>09</month><year>2024</year></pub-date><volume>23</volume><issue>3</issue><issue-title xml:lang="en"/><issue-title xml:lang="ru"/><fpage>158</fpage><lpage>163</lpage><history><date date-type="received" iso-8601-date="2024-04-04"><day>04</day><month>04</month><year>2024</year></date><date date-type="accepted" iso-8601-date="2024-07-27"><day>27</day><month>07</month><year>2024</year></date></history><permissions><copyright-statement xml:lang="en">Copyright ©; 2025, «D. Rogachev NMRCPHOI»</copyright-statement><copyright-statement xml:lang="ru">Copyright ©; 2025, ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России</copyright-statement><copyright-year>2025</copyright-year><copyright-holder xml:lang="en">«D. Rogachev NMRCPHOI»</copyright-holder><copyright-holder xml:lang="ru">ФГБУ «НМИЦ ДГОИ им. Дмитрия Рогачева» Минздрава России</copyright-holder><ali:free_to_read xmlns:ali="http://www.niso.org/schemas/ali/1.0/"/><license><ali:license_ref xmlns:ali="http://www.niso.org/schemas/ali/1.0/">https://creativecommons.org/licenses/by/4.0</ali:license_ref></license></permissions><self-uri xlink:href="https://hemoncim.com/jour/article/view/836">https://hemoncim.com/jour/article/view/836</self-uri><abstract xml:lang="en"><p>Fibrocartilaginous mesenchymoma of the bone is an extremely rare, locally aggressive tumor which is most often found in the long bones of younger patients. Only about 36 cases have been described in the world literature since 1984. Here, we report a rare clinical case of fibrocartilaginous mesenchymoma of the bone in a 13-year-old child. The patient's parents gave consent to the use of their child's data, including photographs, for research purposes and in publications.</p></abstract><trans-abstract xml:lang="ru"><p>Фиброзно-хрящевая мезенхимома кости – крайне редкая локально агрессивная опухоль, чаще всего обнаруживается у молодых пациентов в длинных трубчатых костях. На сегодняшний день в мировой литературе насчитывается около 36 описанных случаев с упоминанием данной патологии, начиная с 1984 г. В данной статье представлен редкий клинический случай фиброзно-хрящевой мезенхимомы кости у девочки 13 лет. Родители пациентки дали согласие на использование информации, в том числе фотографий ребенка, в научных исследованиях и публикациях.</p></trans-abstract><kwd-group xml:lang="en"><kwd>fibrocartilaginous mesenchymoma</kwd><kwd>desmoplastic fibroma</kwd><kwd>fibrocartilaginous dysplasia</kwd></kwd-group><kwd-group xml:lang="ru"><kwd>фиброзно-хрящевая мезенхимома</kwd><kwd>десмопластическая фиброма</kwd><kwd>фибрознохрящевая дисплазия</kwd></kwd-group><funding-group><funding-statement xml:lang="ru">Не указан</funding-statement></funding-group></article-meta></front><body></body><back><ref-list><ref id="B1"><label>1.</label><citation-alternatives><mixed-citation xml:lang="en">Fletcher CD. WHO classification of tumours of soft tissue and bone tumours. 5th ed. Lyon: IARC Press; 2020. pp. 470–1. [Google Scholar]</mixed-citation><mixed-citation xml:lang="ru">Fletcher C.D. WHO classification of tumours of soft tissue and bone tumours. 5th ed. Lyon: IARC Press; 2020. 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