Steatohepatitic variant of hepatocellular carcinoma in a child (a rare clinical case report and a literature review)

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Abstract

Malignant liver tumors are a rare type of pediatric cancer, accounting for 1–2% of all malignant neoplasms in children. Hepatoblastoma is the most common malignant liver tumor, occurring in 80% of cases in children aged 6 months to 3 years. Hepatocellular carcinoma (HCC) usually affects older children, and in adolescents it is more common than hepatoblastoma. Unlike adults, etiological factors for HCC have not been identified in most children. When discussing the histological classification (the 5th edition of the World Health Organization), special attention was drawn to one of the subtypes of HCC – the steatohepatitic variant, which, according to the literature, had never been encountered in children. Here, we present a clinical case of an 11-yearold girl, who was diagnosed with malignant tumor of the right liver lobe. The patient's parents gave consent to the use of their child's data, including photographs, for research purposes and in publications. The diagnosis was made based on the results of a comprehensive diagnostic evaluation, including imaging studies and blood testing for tumor markers. The initial alphafetoprotein level was increased to more than 8000 ng/mL. After successful neoadjuvant multi-agent chemotherapy, the patient underwent surgery involving the resection of hepatic segments V and VI containing the tumor. Histological examination and immunohistochemistry revealed the steatohepatitic variant of HCC. The radicality of the surgery (R0 resection) was confirmed. In some published studies, an association of steatohepatitic HCC (SH-HCC) with obesity and metabolic syndrome is discussed. In others, however, it is suggested that there may be no connection between the development of SH-HCC and obesity or nonalcoholic fatty liver disease. This clinical case report is the first description of SH-HCC in a child. Despite the uniqueness of this case, pediatric oncologists should be aware that the steatohepatitic variant of HCC not associated with obesity or metabolic syndrome can also occur in children. SH-HCC is more likely to result from alterations of common genes or metabolic pathways within the tumor and is an ideal subtype for future genetic studies.

About the authors

T. A. Sharoev

The V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children of the Department of Health of Moscow;
The M.F. Vladimirsky Moscow Regional Research and Clinical Institute (MONIKI);
The Russian Medical Academy of Continuous Professional Education of Ministry of Healthcare of the Russian Federation

Author for correspondence.
Email: timuronco@mail.ru

Timur A. Sharoev, Head of the Scientific Department at the V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children; Professor at the L.A. Durnov Department of Pediatric Oncology of the Russian Medical Academy of Continuous Professional Education of Ministry of Healthcare of the Russian Federation; Professor at the Department of Pediatrics of the Postgraduate Training Faculty of the M.F. Vladimirsky Moscow Regional Research and Clinical Institute (MONIKI)

38 Aviatorov St., 119620 Moscow

Russian Federation

D. K. Nishonov

The V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children of the Department of Health of Moscow

Moscow

Russian Federation

I. S. Mamedov

The V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children of the Department of Health of Moscow

ORCID iD: 0000-0003-0783-2873

Moscow

Russian Federation

S. S. Zhilina

The V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children of the Department of Health of Moscow;
The N.I. Pirogov Russian National Research Medical University of Ministry of Healthcare of the Russian Federation

ORCID iD: 0000-0002-2400-0748

Moscow

Russian Federation

O. A. Perevesentsev

The V.F. Voyno-Yasenetsky Scientific and Practical Center of Specialized Medical Care for Children of the Department of Health of Moscow

ORCID iD: 0000-0002-7070-3209

Moscow

Russian Federation

D. A. Skobeev

The Morozov Children's City Clinical Hospital of the Department of Health of Moscow

ORCID iD: 0000-0001-6446-9201

Moscow

Russian Federation

I. V. Zolkina

Clinic of Novel Medical Technologies ‘ArkhiMed’

ORCID iD: 0000-0003-2117-386X

Moscow

Russian Federation

M. I. Tkacheva

Clinic of Novel Medical Technologies ‘ArkhiMed’

ORCID iD: 0009-0006-6062-9064

Moscow

Russian Federation

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Copyright (c) 2024 Sharoev T.A., Nishonov D.K., Mamedov I.S., Zhilina S.S., Perevesentsev O.A., Skobeev D.A., Zolkina I.V., Tkacheva M.I.

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