Panniculitis-like T-cell lymphoma in children

J. N. Garloeva; Гарлоева Ю. Н.; V. V. Fominyh; Фоминых В. В.; L. N. Shelihova; Шелихова Л. Н.; D. S. Abramov; Абрамов Д. С.; N. V. Myakova; Мякова Н. В.

doi:10.24287/1726-1708-2019-18-1-81-87

Panniculitis-like T-cell lymphoma in children

Authors: Garloeva J.N.¹, Fominyh V.V.¹, Shelihova L.N.¹, Abramov D.S.¹, Myakova N.V.¹
Affiliations:
1. Dmitriy Rogachev National Medical Research Center of Pediatric Hematology, Oncology, Immunology Ministry of Healthcare of Russian Federation
Issue: Vol 18, No 1 (2019)
Pages: 81-87
Section: CLINICAL OBSERVATIONS
Submitted: 21.04.2019
Accepted: 21.04.2019
Published: 21.04.2019
URL: https://hemoncim.com/jour/article/view/229
DOI: https://doi.org/10.24287/1726-1708-2019-18-1-81-87
ID: 229

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Abstract

Subcutaneous panniculitis-like T-cell lymphoma is a rare form of peripheral T-cell lymphoma. The frequency of occurrence of this pathology is 1% of all primary T-cell lymphomas of the skin, at that 20% of all population are children and adolescents, in this way, the percentage of occurrence of this type of tumor in the pediatric population is less than 1%. Given the rarity of pathology, there is no single tactic of therapy and an assessment of its effectiveness. This article presents a review of the literature on the description, diagnosis, and treatment of panniculitis-like T-cell lymphoma. It also presents a clinical case of the development of this type of lymphoma in a 3-year-old child, with a progressive course and subsequent HScT from a haploinentical relative donor.

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